| 引用本文： |
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王芹芹综述,熊伍军审校.多囊肝的病因、诊断及治疗的研究进展[J].同济大学学报（医学版）,2015,36(2):129-132. [点击复制]
- WANG Qin-qin,XIONG Wu-jun.Research progress on etiology,diagnosis and treatment of polycystic liver[J].Journal of Tongji University(Medical Science),2015,36(2):129-132. [点击复制]
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| 摘要: |
| 多囊肝是一种常染色体显性遗传疾病,常与成人多囊肾伴发,早期常无症状,很少影响肝功能,但随病情发展,可出现腹胀、腹痛及腹部包块,影响患者的正常生活。其病因及发病机制尚不明确,目前临床上的治疗方法都不太理想。本研究回顾了近几年国内外有关文献,主要对多囊肝的病因、危险因素、分级、诊断及治疗作一综述,用于指导临床诊断及治疗。 |
| 关键词: 多囊肝 多囊肾 基因突变 |
| DOI：10.16118/j.1008-0392.2015.02.030 |
| 通信作者: |
| 投稿时间：2014-05-20 |
| 录用日期： |
| 基金项目:上海市浦东新区卫生系统重点专科项目(QJ020) |
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| Research progress on etiology,diagnosis and treatment of polycystic liver |
| WANG Qin-qin,XIONG Wu-jun |
| (Dept. of Hepatology, East Hospital, Tongji University, Shanghai 200120, China) |
| Abstract: |
| Polycystic liver disease is an autosomal dominant genetic disease, often associated with adult polycystic kidney disease. The disease is often asymptomatic in the early stage, rarely affects liver function, but with the progression of the disease, there may be bloating, abdominal pain and abdominal mass, affecting normal life of patients. The etiology and pathogenesis are not clear, and the clinical treatments are less desirable. This article reviews the recent literatures published at home and abroad on the main cause, risk factors, classification, diagnosis and treatment of polycystic liver disease. |
| Key words: polycystic liver polycystic kidney disease gene mutation |
